Successful resection of malignant hemangiopericytoma originating from left neck and involving superior vena cava

Background and methods We report a case of a giant malignant hemangiopericytoma in the left neck and involving and growing in left internal jugular, left subclvian, left brachiocephalic vein, superior vena cava (SVC) and occupying part of the right atrium. Tumor was causing severe dyspnea, dysphagia and initial SVC syndrome. A 77-year-old male was admitted to our hospital due to progressive dyspnea and dysphagia. Physical examination present large tumor mass in left supraclavicular and neck region with listening a trill. CT scan explain a large tumor mass started in level of hyoid in left side neck that involve deep veins and expand vessels. Tumor have a arterial blood circulation in SVC. Transthoracic echocardiography showed a mass occupying a space of the right atrium originating from the SVC. Cervicosternotomy used for surgical access. After bluntly removed the tumor from the left neck and ligation of the jugular and subclavian vein proceed to the vascular reconstruction. SVC reconstruction was performed between the right brachiocephalic vein and the right atrial appendage with ringed pericardial graft. Atrial part of tumor was shoved into a SVC. Tumor with vena cava was removed after reconstruction.